Anaesthetic management of patients with mucopolysaccharidosis IV presenting for major orthopaedic surgery.
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Abstract
Mucopolysaccharidosis IV, also known as Morquio-Brailsford syndrome, is an inherited autosomal recessive disorder of mucopolysaccharide metabolism leading to accumulation of keratan sulphate in the connective tissue of multiple organ systems. Based on a case report, the anaesthetic implications for the treatment of patients with MPS IV presenting for major orthopaedic surgery are discussed.
Bibliographical data
| Original language | German |
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| Article number | 6 |
| ISSN | 0001-5172 |
| Publication status | Published - 1999 |
| pubmed | 10408824 |
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