Anaesthetic management of patients with mucopolysaccharidosis IV presenting for major orthopaedic surgery.

  • Hans-Jürgen Bartz
  • L Wiesner
  • F Wappler

Abstract

Mucopolysaccharidosis IV, also known as Morquio-Brailsford syndrome, is an inherited autosomal recessive disorder of mucopolysaccharide metabolism leading to accumulation of keratan sulphate in the connective tissue of multiple organ systems. Based on a case report, the anaesthetic implications for the treatment of patients with MPS IV presenting for major orthopaedic surgery are discussed.

Bibliografische Daten

OriginalspracheDeutsch
Aufsatznummer6
ISSN0001-5172
StatusVeröffentlicht - 1999
pubmed 10408824