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Myocardial function, heart failure and arrhythmia in marfan syndrome: a systematic literature review

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Myocardial function, heart failure and arrhythmia in marfan syndrome: a systematic literature review. / Demolder, Anthony; von Kodolitsch, Yskert; Muiño-Mosquera, Laura; Backer, Julie De.

In: DIAGNOSTICS, Vol. 10, No. 10, 751, 10.2020.

Research output: SCORING: Contribution to journal › SCORING: Review article › Research

Harvard

Demolder, A, von Kodolitsch, Y, Muiño-Mosquera, L & Backer, JD 2020, 'Myocardial function, heart failure and arrhythmia in marfan syndrome: a systematic literature review', DIAGNOSTICS, vol. 10, no. 10, 751. https://doi.org/10.3390/diagnostics10100751

APA

Demolder, A., von Kodolitsch, Y., Muiño-Mosquera, L., & Backer, J. D. (2020). Myocardial function, heart failure and arrhythmia in marfan syndrome: a systematic literature review. DIAGNOSTICS, 10(10), [751]. https://doi.org/10.3390/diagnostics10100751

Vancouver

Demolder A, von Kodolitsch Y, Muiño-Mosquera L, Backer JD. Myocardial function, heart failure and arrhythmia in marfan syndrome: a systematic literature review. DIAGNOSTICS. 2020 Oct;10(10). 751. https://doi.org/10.3390/diagnostics10100751

Bibtex

@article{eae66a3cbbff4fff9a49e67890a8160e,
title = "Myocardial function, heart failure and arrhythmia in marfan syndrome: a systematic literature review",
abstract = "Marfan syndrome (MFS) is a heritable systemic connective tissue disease with important cardiovascular involvement, including aortic root dilatation and mitral valve prolapse. Life expectancy in patients with MFS is mainly determined by cardiovascular complications, among which aortic dissection or rupture are most dreaded. In recent years, heart failure and ventricular arrhythmia have drawn attention as extra-aortic cardiovascular manifestations and as additional reported causes of death. Imaging studies have provided data supporting a primary myocardial impairment in the absence of valvular disease or cardiovascular surgery, while studies using ambulatory ECG have demonstrated an increased susceptibility to ventricular arrhythmia. In this paper, current literature was reviewed in order to provide insights in characteristics, pathophysiology and evolution of myocardial function, heart failure and ventricular arrhythmia in MFS.",
keywords = "Heart failure, Marfan syndrome, Myocardial, Ventricular arrhythmia",
author = "Anthony Demolder and {von Kodolitsch}, Yskert and Laura Mui{\~n}o-Mosquera and Backer, {Julie De}",
note = "Publisher Copyright: {\textcopyright} 2020 by the authors.",
year = "2020",
month = oct,
doi = "10.3390/diagnostics10100751",
language = "English",
volume = "10",
journal = "DIAGNOSTICS",
issn = "2075-4418",
publisher = "MDPI AG",
number = "10",

}

RIS

TY - JOUR

T1 - Myocardial function, heart failure and arrhythmia in marfan syndrome: a systematic literature review

AU - Demolder, Anthony

AU - von Kodolitsch, Yskert

AU - Muiño-Mosquera, Laura

AU - Backer, Julie De

N1 - Publisher Copyright: © 2020 by the authors.

PY - 2020/10

Y1 - 2020/10

N2 - Marfan syndrome (MFS) is a heritable systemic connective tissue disease with important cardiovascular involvement, including aortic root dilatation and mitral valve prolapse. Life expectancy in patients with MFS is mainly determined by cardiovascular complications, among which aortic dissection or rupture are most dreaded. In recent years, heart failure and ventricular arrhythmia have drawn attention as extra-aortic cardiovascular manifestations and as additional reported causes of death. Imaging studies have provided data supporting a primary myocardial impairment in the absence of valvular disease or cardiovascular surgery, while studies using ambulatory ECG have demonstrated an increased susceptibility to ventricular arrhythmia. In this paper, current literature was reviewed in order to provide insights in characteristics, pathophysiology and evolution of myocardial function, heart failure and ventricular arrhythmia in MFS.

AB - Marfan syndrome (MFS) is a heritable systemic connective tissue disease with important cardiovascular involvement, including aortic root dilatation and mitral valve prolapse. Life expectancy in patients with MFS is mainly determined by cardiovascular complications, among which aortic dissection or rupture are most dreaded. In recent years, heart failure and ventricular arrhythmia have drawn attention as extra-aortic cardiovascular manifestations and as additional reported causes of death. Imaging studies have provided data supporting a primary myocardial impairment in the absence of valvular disease or cardiovascular surgery, while studies using ambulatory ECG have demonstrated an increased susceptibility to ventricular arrhythmia. In this paper, current literature was reviewed in order to provide insights in characteristics, pathophysiology and evolution of myocardial function, heart failure and ventricular arrhythmia in MFS.

KW - Heart failure

KW - Marfan syndrome

KW - Myocardial

KW - Ventricular arrhythmia

UR - http://www.scopus.com/inward/record.url?scp=85092235409&partnerID=8YFLogxK

U2 - 10.3390/diagnostics10100751

DO - 10.3390/diagnostics10100751

M3 - SCORING: Review article

AN - SCOPUS:85092235409

VL - 10

JO - DIAGNOSTICS

JF - DIAGNOSTICS

SN - 2075-4418

IS - 10

M1 - 751

ER -