Management of Pentalogy of Cantrell with complete ectopia cordis and Double Outlet Right Ventricle

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Management of Pentalogy of Cantrell with complete ectopia cordis and Double Outlet Right Ventricle. / Harring, Gesa; Weil, Joachim; Thiel, Christian; Schmelzle, Rainer; Müller, Götz.

In: CONGENIT ANOM, Vol. 55, No. 2, 2015, p. 121-123.

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@article{13c3c8c097b0486b9bb41af791441227,
title = "Management of Pentalogy of Cantrell with complete ectopia cordis and Double Outlet Right Ventricle",
abstract = "Pentalogy of Cantrell (P.o.C.) is a rare congenital midline defect. We present a case and its treatment of P.o.C. with complete ectopia cordis and congenital heart disease. Postnatally the congenital heart defect was surgically corrected and the ectopic heart was covered by musculous mobilized flap. Due to cephalic orientation of the heart and limited intrathoracic space, replacement of the heart into the thoracic cavity was initially not performed. After 11 years of follow up our patient now is without relevant limitations solely wearing a thoracic shelter. This case elucidates the complexity of further management. The potential risk of disastrous hemodynamic compromise by intrathoracic shift is to compare with the limited safety of the ectopic heart.",
author = "Gesa Harring and Joachim Weil and Christian Thiel and Rainer Schmelzle and G{\"o}tz M{\"u}ller",
note = "This article is protected by copyright. All rights reserved.",
year = "2015",
doi = "10.1111/cga.12096",
language = "English",
volume = "55",
pages = "121--123",
journal = "CONGENIT ANOM",
issn = "0914-3505",
publisher = "Wiley-Blackwell",
number = "2",

}

RIS

TY - JOUR

T1 - Management of Pentalogy of Cantrell with complete ectopia cordis and Double Outlet Right Ventricle

AU - Harring, Gesa

AU - Weil, Joachim

AU - Thiel, Christian

AU - Schmelzle, Rainer

AU - Müller, Götz

N1 - This article is protected by copyright. All rights reserved.

PY - 2015

Y1 - 2015

N2 - Pentalogy of Cantrell (P.o.C.) is a rare congenital midline defect. We present a case and its treatment of P.o.C. with complete ectopia cordis and congenital heart disease. Postnatally the congenital heart defect was surgically corrected and the ectopic heart was covered by musculous mobilized flap. Due to cephalic orientation of the heart and limited intrathoracic space, replacement of the heart into the thoracic cavity was initially not performed. After 11 years of follow up our patient now is without relevant limitations solely wearing a thoracic shelter. This case elucidates the complexity of further management. The potential risk of disastrous hemodynamic compromise by intrathoracic shift is to compare with the limited safety of the ectopic heart.

AB - Pentalogy of Cantrell (P.o.C.) is a rare congenital midline defect. We present a case and its treatment of P.o.C. with complete ectopia cordis and congenital heart disease. Postnatally the congenital heart defect was surgically corrected and the ectopic heart was covered by musculous mobilized flap. Due to cephalic orientation of the heart and limited intrathoracic space, replacement of the heart into the thoracic cavity was initially not performed. After 11 years of follow up our patient now is without relevant limitations solely wearing a thoracic shelter. This case elucidates the complexity of further management. The potential risk of disastrous hemodynamic compromise by intrathoracic shift is to compare with the limited safety of the ectopic heart.

U2 - 10.1111/cga.12096

DO - 10.1111/cga.12096

M3 - SCORING: Journal article

C2 - 25385246

VL - 55

SP - 121

EP - 123

JO - CONGENIT ANOM

JF - CONGENIT ANOM

SN - 0914-3505

IS - 2

ER -