Dermal cylindroma of the scalp (turban tumour) and subjacent calvarian defects
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Dermal cylindroma of the scalp (turban tumour) and subjacent calvarian defects. / Friedrich, Reinhard E.
in: ANTICANCER RES, Jahrgang 30, Nr. 5, 01.05.2010, S. 1793-7.Publikationen: SCORING: Beitrag in Fachzeitschrift/Zeitung › SCORING: Zeitschriftenaufsatz › Forschung › Begutachtung
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TY - JOUR
T1 - Dermal cylindroma of the scalp (turban tumour) and subjacent calvarian defects
AU - Friedrich, Reinhard E
PY - 2010/5/1
Y1 - 2010/5/1
N2 - This case report describes the diagnosis and therapy of a patient with a 40-year history of multiple potato-like tumours growing in the head and neck region. The tumour proved to be a cylindroma, associated with calvarian defects. Further facial tumours were diagnosed as trichoepitheliomas. This association of findings was pathognomonic for Brooke-Spiegler's syndrome. Complete work-up of the resection specimen excluded any malignant transformation of the tumour. A long lasting history of cylindroma and evidence for bone destruction, not associated with a malignant transformation, is extremely rare in Brooke-Spiegler's syndrome.
AB - This case report describes the diagnosis and therapy of a patient with a 40-year history of multiple potato-like tumours growing in the head and neck region. The tumour proved to be a cylindroma, associated with calvarian defects. Further facial tumours were diagnosed as trichoepitheliomas. This association of findings was pathognomonic for Brooke-Spiegler's syndrome. Complete work-up of the resection specimen excluded any malignant transformation of the tumour. A long lasting history of cylindroma and evidence for bone destruction, not associated with a malignant transformation, is extremely rare in Brooke-Spiegler's syndrome.
KW - Aged
KW - Angiography
KW - Biopsy
KW - Carcinoma, Adenoid Cystic
KW - Carotid Arteries
KW - Female
KW - Head and Neck Neoplasms
KW - Humans
KW - Magnetic Resonance Imaging
KW - Scalp
KW - Skin
KW - Skin Neoplasms
KW - Syndrome
KW - Treatment Outcome
M3 - SCORING: Journal article
C2 - 20592381
VL - 30
SP - 1793
EP - 1797
JO - ANTICANCER RES
JF - ANTICANCER RES
SN - 0250-7005
IS - 5
ER -